Data di Pubblicazione:
2020
Citazione:
Therapeutic management of ventricular arrhythmias in Andersen-Tawil syndrome / S. Maffè, P. Paffoni, L. Bergamasco, P. Dellavesa, F. Zenone, L. Baduena, N. Franchetti Pardo, G. Careri, E. Facchini, V. Sansone, U. Parravicini. - In: JOURNAL OF ELECTROCARDIOLOGY. - ISSN 0022-0736. - 58(2020 Feb), pp. 37-42. [10.1016/j.jelectrocard.2019.10.009]
Abstract:
Andersen-Tawil Syndrome (ATS) is a rare periodic paralysis with typical skeletal and neuromuscular features. Cardiac involvement may range from asymptomatic ventricular arrhythmias to sudden death. Its management remains challenging and the choice between antiarrhythmic drug therapy and implantable cardioverter defibrillator (ICD) is not simple. We present a case of ATS patient with episodes of bidirectional ventricular tachycardia, well controlled by flecainide therapy initially, which in particular conditions of fever and hypokaliemia had a cardiac arrest with ventricular fibrillation, with neurological sequelae and need of an ICD implant. A review of the therapeutic management of this disease is presented.
Tipologia IRIS:
01 - Articolo su periodico
Keywords:
Andersen-Tawil syndrome; Bidirectional ventricular tachycardia; Subcutaneous implantable cardioverter defibrillator
Elenco autori:
S. Maffè, P. Paffoni, L. Bergamasco, P. Dellavesa, F. Zenone, L. Baduena, N. Franchetti Pardo, G. Careri, E. Facchini, V. Sansone, U. Parravicini
Link alla scheda completa: