Data di Pubblicazione:
2016
Citazione:
Sézary Syndrome in a 17-Year-Old Boy : Clinicopathologic Features and Genomic Profile / S. Alberti Violetti, P. Vezzoli, L. Corti, D. Fanoni, V. Merlo, L. Venegoni, A. Reseghetti, E. Berti. - In: PEDIATRIC DERMATOLOGY. - ISSN 0736-8046. - 33:5(2016 Sep), pp. e318-e321. [10.1111/pde.12930]
Abstract:
We describe the case of a 17-year-old Hispanic boy who had had erythroderma and diffuse lymphadenopathy for approximately 6 months. A diagnosis of Sézary syndrome was made on the basis of the histologic features of the skin; the presence of the same T-cell clone on the skin, blood, and bone marrow; and the high CD4+ lymphocyte count with an aberrant phenotype in peripheral blood; bone marrow involvement was also present. The patient was treated with systemic gemcitabine and achieved partial remission.
Tipologia IRIS:
01 - Articolo su periodico
Keywords:
2708; pediatrics, perinatology and child health
Elenco autori:
S. Alberti Violetti, P. Vezzoli, L. Corti, D. Fanoni, V. Merlo, L. Venegoni, A. Reseghetti, E. Berti
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