Effects of long-chain polyunsaturated fatty acid supplementation on fatty acid status and visual function in treated children with hyperphenylalaninemia
Articolo
Data di Pubblicazione:
2000
Citazione:
Effects of long-chain polyunsaturated fatty acid supplementation on fatty acid status and visual function in treated children with hyperphenylalaninemia / C. Agostoni, N. Massetto, G. Biasucci, A. Rottoli, M. Bonvissuto, M. G. Bruzzese, M. Giovannini, E. Riva. - In: THE JOURNAL OF PEDIATRICS. - ISSN 0022-3476. - 137:4(2000 Oct), pp. 504-509.
Abstract:
Children with phenylalanine-hydroxylase deficiency (type-I hyperphenylalaninemia, HPA) follow a low-phenylalanine diet, severely restricted in animal foods and long-chain polyunsaturated fatty acids (LCPUFA). Consequently, they have a poor LCPUFA status, particularly for docosahexaenoic acid (DHA). DHA is relevant to visual and neural development.
Tipologia IRIS:
01 - Articolo su periodico
Keywords:
Fatty Acids, Unsaturated ; Double-Blind Method ; Humans ; Phenylalanine Hydroxylase ; Vision, Ocular ; Fatty Acids ; Child ; Dietary Supplements ; Phenylalanine ; Male ; Female
Elenco autori:
C. Agostoni, N. Massetto, G. Biasucci, A. Rottoli, M. Bonvissuto, M. G. Bruzzese, M. Giovannini, E. Riva
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