Data di Pubblicazione:
1990
Citazione:
POEMS syndrome with IgA lambda monoclonal gammopathy / A. Costa, G. Barosi, G. Piccolo, E. Nobile-Orazio, N. L. Liberato, E. Ascari. - In: HAEMATOLOGICA. - ISSN 0390-6078. - 75:2(1990), pp. 170-2-172.
Abstract:
The various association of polyneuropathy, organomegaly, endocrinopathy, monoclonal protein and skin changes has been called the POEMS syndrome. Herein we report a case in which all the typical clinical and laboratory findings of the POEMS syndrome were present. We emphasize as the most striking features of our case the following: the similarity with scleroderma, the peripheral nerve demyelination without the presence of antibodies against nerve components, the occurrence of an IgA lambda monoclonal gammopathy and Castleman-like features at a single enlarged lymph node. To our knowledge, this is the first such case reported in Italy.
Tipologia IRIS:
01 - Articolo su periodico
Keywords:
Immunoglobulin A; Immunoglobulin lambda-Chains; Skin Diseases; Syndrome; Humans; Nervous System Diseases; Endocrine System Diseases; Paraproteinemias; Middle Aged; Male
Elenco autori:
A. Costa, G. Barosi, G. Piccolo, E. Nobile-Orazio, N. L. Liberato, E. Ascari
Link alla scheda completa: