Data di Pubblicazione:
2011
Citazione:
Steroid-responsive Hashimoto encephalopathy mimicking Creutzfeldt-Jakob disease / D. Santoro, I. Colombo, I. Ghione, L. Peverelli, N. Bresolin, M. Sciacco, A. Prelle. - In: NEUROLOGICAL SCIENCES. - ISSN 1590-1874. - 32:4(2011 Aug 11), pp. 719-722.
Abstract:
Hashimoto's encephalopathy (HE) is a rare neurological disorder with a heterogeneous group of neurological symptoms associated with high titres of anti-thyroid antibodies. Clinical manifestations may include encephalopathic features such as seizures, behavioural and psychiatric manifestations, movement disorders and coma. The objective of this presentation is to describe a patient with this rare and controversial clinical syndrome mimicking Creutzfeldt-Jakob disease, associated with a Hashimoto euthyroid thyroiditis and with a significant response to high dose intravenous prednisone. The responsiveness of this syndrome to steroids suggests that this disorder involves immune pathogenic mechanisms, as previous reviews reported.
Tipologia IRIS:
01 - Articolo su periodico
Keywords:
encephalopathy; Hashimoto; anti-thyroid antibodies; steroids
Elenco autori:
D. Santoro, I. Colombo, I. Ghione, L. Peverelli, N. Bresolin, M. Sciacco, A. Prelle
Link alla scheda completa: